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Dernières publications
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Valentina Taglietti, Kaouthar Kefi, Lea Rivera, Oriane Bergiers, Nastasia Cardone, et al.. Thyroid-stimulating hormone receptor signaling restores skeletal muscle stem cell regeneration in rats with muscular dystrophy. Science Translational Medicine, 2023, 15 (685), ⟨10.1126/scitranslmed.add5275⟩. ⟨hal-04150315⟩
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A. Morin, Amalia Stantzou, Olga N. Petrova, John C.W. Hildyard, T. Tensorer, et al.. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle. Proceedings of the National Academy of Sciences of the United States of America, 2023, 120 (2), ⟨10.1073/pnas.2206324120⟩. ⟨hal-04122777⟩
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Valentina Taglietti, Kaouthar Kefi, Iwona Bronisz-Budzyńska, Busra Mirciloglu, Mathilde Rodrigues, et al.. Duchenne muscular dystrophy trajectory in R-DMDdel52 preclinical rat model identifies COMP as biomarker of fibrosis. Acta Neuropathologica Communications, 2022, 10 (1), ⟨10.1186/s40478-022-01355-2⟩. ⟨hal-03828280⟩
Chiffres clés
47
Publications avec texte intégral
Open Access
73 %
Mots clés
Ex-vivo
Homeostasis
CaV subunits
CaVβs
LKB1
Epigenetics
Diseases
Dystrophie musculaire de Becker
Long noncoding RNA
DMD
Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS
Muscular dystrophy
Metabolism
Mitochondrial fission
Muscle Strength
Knockout
Base Sequence
Human Umbilical Vein Endothelial Cells
Becker muscular dystrophy BMD
Inbred C57BL
Inhibitors
Gene Expression Regulation/drug effects
Cultured
Autophagy
Myotendinous junction
Muscular Dystrophy
Morphogenesis
CD38
Cardiomyopathy
Humans
Centronuclear myopathy
Muscle Biology
Mice
Muscles/physiopathology
Cachexia
BMD
Dystrophin central domain
Muscle development
Cardiomyopathie
DMO
Clinical trials
Duchenne muscular dystrophy DMD
Dystrophie Musculaire de Duchenne DMD
Dystrophy
Calcium
Activin Receptors
Invivo
Myogenesis
Calcium Channels
MES
Multi exon skipping
Allele‐specific silencing therapy
LncRNA
Immunoglobulin Fc Fragments/pharmacology
Dystrophin
Becker muscular dystrophy
DHPR α1S
Animals
MiARN
Muscle
Génomique
Multi resolution modeling
Male
Molecular Sequence Data
Dystrophie Musculaire de Becker BMD
Dystrophin-EGFP
NAD+
Delivery
Molecular docking
Dynamin 2
Becker BMD muscular dystrophy
NNOS
Cell homeostasis
Skeletal muscle
Muscular Atrophy
L-Type
Duchenne DMD dystrophy
Exon skipping
Cell Line
Genomic
Hear
Multiresolution modeling
Cells
Gene expression
Cell Biology
Hepatocellular carcinoma
CTNNB1
Duchenne muscular dystrophy
Inbred mdx
Gene modifiers
Drp1
Energy Metabolism/drug effects
Long QT
Antisense oligonucleotides
Dystrophine
LncARN
Modificateurs de gènes
Mdx mouse
Liver
Animal/physiopathology